ATP2B2 (ATPase Plasma Membrane Ca²⁺ Transporting 2) is a gene that encodes a calcium pump responsible for regulating intracellular calcium levels. This pump plays a vital role in various cellular processes such as signal transduction, muscle contraction, and neurotransmitter release. Mutations in ATP2B2 have been linked to hearing loss and vestibular disorders, emphasising its importance in maintaining calcium balance within sensory hair cells essential for hearing and balance.